Segmental muscular atrophy of the distal upper extremity (Hirayama disease): An atypical case with anterior dural detachment

Martijn Ruben Meijerink*, Jonas Castelijns, Frederik Barkhof

*Corresponding author for this work

Research output: Contribution to journalArticleAcademicpeer-review


Segmental non-progressive spinal muscular atrophy of the upper extremity, also known as Hirayama disease (HD), is a disorder seen mainly in young male patients of Asian ancestry. On MRI loss-of-attachment between the posterior dural sac and adjacent lamina has been described as the only significantly important predictor of HD. We herein present a patient with HD who showed an atypical anterior detachment of the dura mater from the adjacent vertebral body.

Original languageEnglish
Pages (from-to)e53-e55
JournalEuropean Journal of Radiology Extra
Issue number2
Publication statusPublished - 1 Nov 2009

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